Faculty Bibliography

Echocardiography is an extraordinarily useful imaging technique in fetuses, infants, children, and adolescents. Recent technologic innovations have expanded its versatility in the pediatrie population. However, limited societal resources, limitations inherent to ultrasound imaging, and numerous imaging options even within the field of pediatrie echocardiography necessitate the discriminate and thoughtful use of echocardiography in children. The clinical assessment remains a critical prelude to echocardiographic examination of the pediatrie cardiovascular system

We assessed how well transesophageal echocardiography (TEE) images the left pulmonary artery (LPA) in congenital heart disease (CHD). Seventy-nine consecutive patients with CHD were studied. Ideal imaging displayed the mid to distal LPA from the takeoff of the upper lobe artery through the second bifurcation. Imaging quality was graded from 1 (excellent) to 5 (not visualized). Imaging quality was excellent in 8 (10%) patients, good in 25 (32%), fair in 23 (29%), and poor in 12 (15%); the LPA was not visualized in 11 (14%) patients. Imaging grade averaged 2.9 +/- 1.2 (SD) and correlated poorly with weight (r = 0.24) but was better in patients without prior operation (grade 2.8 vs 3.3, P <.05). In 2 patients, TEE showed residual stenosis. Thus informative LPA imaging by TEE can be achieved in many patients with CHD and has the potential to change intraoperative or postoperative treatment

Echocardiography is an extraordinarily useful imaging technique in fetuses, infants, children, and adolescents. Recent technologic innovations have expanded its versatility in the pediatric population. However, limited societal resources, limitations inherent to ultrasound imaging, and numerous imaging options even within the field of pediatric echocardiography necessitate the discriminate and thoughtful use of echocardiography in children. The clinical assessment remains a critical prelude to echocardiographic examination of the pediatric cardiovascular system

The shorthand rule that the QTc will be normal if the QT interval is <1/2 the RR interval was mathematically validated. The rule was found to be applicable and useful, provided the heart rate is more than approximately 70 beats/min

BACKGROUND: There is often substantial mismatch between the diameters of the pulmonary and aortic anuli in young patients with systemic outflow tract disease. To implant the autologous pulmonary valve in the aortic position under such circumstances, it is necessary to adapt the geometry of the systemic outflow tract. The effects of such adaptations on autograft function in children are not well known. METHODS: To determine factors predictive of autograft regurgitation, we analyzed 41 cases of children who have undergone the Ross procedure. The diameter of the pulmonary valve was greater (by at least 3 mm) than that of the aortic valve in 20 cases, equal (within 2 mm) in 12 cases, and less (by at least 3 mm) in nine cases, with differences ranging from +10 to -12 mm. In 12 patients with a larger pulmonary anulus, aortoventriculoplasty was used to correct the mismatch. In patients with a larger aortic anulus, the mismatch was corrected by gradual adjustment along the circumference of the autograft, rather than by tailoring of the native aortic anulus. RESULTS: At follow-up (median 31 months), two patients had undergone reoperation on the neoaortic valve for moderate regurgitation. In the remaining 38 cases, autograft regurgitation was as follows: none or trivial in 30, mild in seven, and moderate in one. There was no correlation between regurgitation and age, geometric mismatch, or previous or concurrent procedures. CONCLUSIONS: Subtle technical factors that may result in distortion of the valve complex are probably more important determinants of autograft regurgitation than are indication for repair, geometric mismatch, or previous or concomitant outflow tract procedures. Significant mismatch of the semilunar anuli is not a contraindication to the Ross procedure in children

OBJECTIVES: We modeled the utility of preoperative potential left ventricular (LV) volume in predicting postoperative volume in conditions causing LV compression. BACKGROUND: With right ventricular (RV) overload lesions, LV 'hypoplasia' may be primarily due to compression by reverse septal bowing. If so, preoperative potential LV volume should correspond 1:1 with postoperative volume. The potential volume for a given endocardial circumference can be calculated from the maximal potential cross-sectional area (where A = circumference(2)/4pi) and LV length. METHODS: We studied echocardiographic variables from 22 patients with RV overload lesions perioperatively. RESULTS: Preoperative LV volume was 15.0 +/- 7.1 ml/m2 (59% of patients had a volume <15 ml/m2); potential volume was 20.0 +/- 9.8 ml/m2. Postoperative volume increased to 28.2 +/- 8.6 ml/m2 (100% of patients had a volume >15 ml/m2). Preoperative potential volume correlated well with, but generally underestimated, postoperative volume (r = 0.75, p < 0.0001). Postoperative increases in both LV circumference and length contributed to this discrepancy. CONCLUSIONS: In RV overload lesions, LV 'hypoplasia' is primarily due not to compression; rather it is due to underfilling. Even 'hypoplastic' ventricles can achieve an adequate cavity after operation normalizes loading conditions. Both true and potential preoperative volume can predict postoperative volume well. However, potential volume, which is less prone to underestimating ventricular adequacy, may better help to determine suitability for biventricular repair in lesions of RV overload associated with a 'hypoplastic' LV